Transcript Document
GRAVES’ ORBITOPATHY
LARRY H ALLEN
IVEY EYE INSTITUTE-UWO
LONDON ONTARIO
GRAVES’ ORBITOPATHY
GRAVES’ ORBITOPATHY
WORLDWIDE INCIDENCE
SMOKING
RI 131
THERAPY
GRAVES’ Orbitopathy
Assumed to be Autoimmune.
Fibroblast most likely target cell with subpopulations to include adipose cells, GAGS
production and Cytokine release.
Target sites appear to in the reto-orbital
tissue most likely the EOM.
Unclear association with the thyroid .
Ophthalmopathy andThyroid
status
40% Concurrent Hyperthyroid
20% Ophthalmopathy Before Hyperthyroid
20%Ophthalmopathy After Hyperthyroid
15-20% Ophthalmopathy Within 6 Months
of each other Before or After Diagnosis
Usually Clinical Signs Preceed CT/MR/US
Findings
Investigations
TSH, Free T4, Thyroid Antibodies.
No association between Thyroid antibodies
and disease severity nor progression.
Pre- tibial Dermopathy is often associated
with more severe disease.
10% of Graves’ patients are Euthyroid.75%
may convert to abnormal Thyroid < 2 yrs.
GRAVES’
Worldwide decrease in incidence EXCEPT
in Eastern European countries where there
is an increase of 30% and an increase in
SMOKING of about 30%!
European survey showed same or decreased
incidence in 85% of respondents.12% of
respondents indicated an increase and were
from those in E. Euorpean areas.
GRAVES’ AND CIGS
Cleaners in Amsterdam Thyroid clinic complained
why this clinic had so many cigs to clean up. 1st
association!!
60% Grave’s smokers: 20% gen . Population:
MAYO study 40% smokers.
Cig smoking ass. with delayed response to steroid
and RTX therapy.Therapy longer in cig smokers
and lack of response to therapy higher.
GRAVES’
Steroid Tx. for optic neuropathy in 1 study
showed results to be better in non smokers.
94% vs 68% better for non smoker grp.
Cig smokers also have a higher Recur and
Relapse rate of Hyperthyroid state.
Cig smoking one of the major risk factor s
and is MODIFIABLE !!!
GRAVES’ R I
R I Tx. May aggravate the orbitopathy.
Ablation of the thyroid liberates Ab that
may increase the immune response in the
orbit.
Studies show an increase in blood levels of
TSHR Ab after R I
Higher levels in smokers!
GRAVES’
One study show R I alone vs Oral vs Sx.
That aggravation seen in 35%;16%;12%.
Bartalena showed R I alone vs R I + oral
steroid saw progression of 15% vs 0%.
However many feel that early ablative Tx
better overall.? Is this a factor in the
reduction in incidence in some countries?
GRAVE’S R I THERAPY
Suggested Tx Timetable In General.
Oral Tx to stabilze thyroid for 6/12.
Mild inflammation R I alone.
Moderate to severe R I+steroid for 6-8wk.
Treat hypothyroid state early.
Reduce or stop smoking.
Some centers treat all with steroid+R I.
Orbitopathy and R I ?
Does R I therapy
cause a progression in
of Graves”
Orbitopathy
YES, in a definite
proportion of patients
(about 15-20%)
Orbitopathy and R I ?
Are there risk factors
for progression of the
Orbitopathy after R I
therapy
YES,Smoking,Hypert
hyroid severity, Late
correction of post-R I
Hypothyroid state, and
highTRAb levels
Orbitopathy and R I ?
Can progression of
Graves’ Orbitopathy
be prevented
YES. With oral
Steroid Prophylaxis
Orbitopathy and R I ?
Are Steroid Dose,
Timing of the
initiation of therapy
after R I, and Duration
of therapy well
defined
NO
Orbitopathy and R I ?
Should All patients
given R I therapy be
given Steroid
Prophylaxis
Steroid Prophylaxis
may be avoided in
patients with absent or
inactive Orbitopathy
provided other risk
factors are Absent ie
Smoking , Orbital
inflammation etc.
GRAVES’ THERAPY
Severe disease or O N compression
IV steroid better than oral but more sideeffects.Steroid often work better with other antiinflammatory agents ex. Cyclosporin but again
S.E. to be considered.Cambridge Protocol
reduction in Sx intervention (EYE 2006)
Variable results with local steroids and other meds
eg., somatostatin analogs,Immunosupressants.
Biologics ie Rituximab and others
GRAVES’ RTX
Radition of orbit and retro-orbital tissue
controversial.
Mayo study no benefit:1 Dutch study
inconclusive:Italian grp feel helpful in 60%
soft tissue changes.
No study ON compreesion and RTX
LHA soft tis. 60% have had good results
with RTX/steroid and ON disease.
GRAVES ‘ Therapy
Surgical Orbital Decompression to enlarge
the Orbit and allow for expansion of the
enlarged EOM bellies into the Sinus area
and thus reduce the Optic Nerve
Compression and Orbital Congestion.
Not without its problems ie variable amts of
decompression,Diplopia , reduction in
Proptosis
GRAVES THERAPY
Should Anti –Smoking therapy and
Campaigns be more aggresively applied to
patients with Graves’ Disease.
Case reports of Graves’ disease improving
after cessation of SMOKING only.
GRAVES’
GRAVES’
GRAVES’
GRAVES’
GRAVES’ DISEASE
THE PUZZLE CONTINUES
ACNE ROSACEA
OCULAR ROSACEA
ACNE ROSACEA
Chronic skin disorder. Middle age(30-60).
Idiopathic in origin affecting fair skin,fair
hair individuals 1*.
Ocular Rosacea inflammatory in the clinical
setting.
Ass. with increased levels of IL-1a and
MMP. Bacterial lipases also a factor.
OCULAR ROSACEA
Tetracyclines inhibit MMP’s and lid
bacterial lipase production thus reducing
free fatty acids in tear film.
Tetracyclines will improne tear BUT.
Most studies with tetra. involve cutaneous
AR .Ocular R Tx an assumed extension.
Tetra. Reduce bacterial flora of eyelids.
OCULAR ROSACEA
Tetra. 2*reduce lipases and FFA which are
toxic to cornea and also improve the tear
BUT.
Reduce neutrophil chemotactic factors and
lid inflammation .
Rosacea associated with an increased
prevalence in chalazions,recurrance,and
multiplicity.LHA study AR 48% of cases.
OCULAR ROSACEA
Thought to be under recognized by Ophthal.
Tx is prolonged.High patient compliance is
needed.Systemic and local Tx required.
Clinically ocular Rosacea more
inflammatory than infectious-LHA.
Tx with Tetra’s,Minocycline,Doxycycline
oral.TopicalAb-steroid ung beneficial.
A R THERAPY
Doxy.50-100 mg bid for 2 wks then once
daily 2-3/12 Cycles of 3-6/12, on –off.
Mino.50-100 mg similar fashion. Mino
more anti-inflamm. More sideffects.
S.E. GIT,Photosensitive,yeast infx.
Topical steroid +/- Ab. ,2-3 wks to settle.
Lid hygiene
A R
2 WEEK INTERVAL
FLOPPY EYELID SYNDROME
FLOPPY LID
Flaccid lid tissue. Ant. surface symptoms.
Tarsus Velvet papillary appearance.
Lash ptosis often seen before lid gets floppy
Lid laxity Upper>lower lid or canthus.
Middle age,M>F,LARGE,sleep prone.
Ass. Sleep Apnea in 8%.
Sleep Apnea ass. 2% Floppy lid.
FLOPPY LIDS
Sleep Apnea ass. with BP,Arrhythmia.
3x increase in MVA
Tx. includes shield in PM initially with lid
tightening as Sx difinitive therapy.
Sleep lab for Dx. and CPAP to reverse
apnea. ? Other TX modalities of value.
Diet and WT loss beneficial.
FLOPPY LID
FLOPPY LID
LASH PTOSIS
UPDATE
THANK YOU for the opportunity to
participate in this Update In Ophthalmology
and Medicine , to the Planning Committee ,
and to Natalie for her administrative
expertise.